FVII deficiency is a rare coagulation disorder. A limited number of patients are found in
most treatment centres and countries. Treatment demands vary considerably amongst FVII
deficient patients. Therefore, regular clinical studies will meet with recruitment problems
in this particular patient population. The present study intends to elucidate the bleeding
patterns in a well-defined collective of FVII deficiency patients who are carefully
characterised, to document the actual use of different treatment modalities in different
subgroups and to evaluate the efficacy and safety of current available treatment modalities
in bleedings, surgery and prophylaxis. The purpose is to gain some evidence based knowledge
of treatment of patients with FVII deficiency - an area where treatment decisions are made
more on personal clinical experience than on consolidated clinical evidence.
This study intends to register treatment practices as they are actually performed - in a
structured and documented way.